KLIPPEL-TRENAUNAY-WEBER SYNDROME
Abstract:
Klippel-Trenaunay syndrome (KTS) is a congenital venous malformation that is characterized
by the triad: varicose veins (generally affecting a single leg), hypertrophy of the affected limb and portwine
stain. Without treatment, the patients with KTS may develop chronic venous insufficiency with
ulceration, massive bleeding, thrombophlebitis, pulmonary emboli, etc. In Parkes-Weber syndrome we
can find arteriovenous malformations with fistulas. Some authors combine these 2 clinical entities in
Klippel-Trenaunay-Weber syndrome. Establishing a correct diagnosis by assessing the existence of
arteriovenous shunts and the types of this malformations as well as their severity, is important. We
present 2 patients diagnosed in the Dermatology Department of the Clinical Hospital of Sibiu with
Klippel-Trenaunay-Weber syndrome, complicated with repeated bleeding, undiagnosed for 12 years,
respectively 20 years.
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